Which failure mode becomes likely when a patient with a mutation affecting intestinal biotinidase experiences a biotin deficiency?

💡 Explanation

Biotin is a crucial cofactor for carboxylase enzymes involved in fatty acid synthesis. A biotinidase deficiency prevents biotin recycling, leading to impaired carboxylase activity; therefore, fatty acid synthesis is disrupted rather than enhanced nerve function because biotin’s primary role centers on metabolic processes.

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